Lymphangioleiomyomatosis and pulmonary Langerhans cell histiocytosis

The journal European Respiratory Review has published an article about Lymphangioleiomyomatosis (LAM) and pulmonary Langerhans cell histiocytosis (PLCH). LAM and PLCH are rare diseases that lead to progressive cystic destruction of the lungs. Despite their distinctive characteristics, these diseases share several features. In this review, the recent advances in the understanding of the molecular pathogenesis, as well as the current and most promising biomarkers and therapeutic approaches, are described.  The full-text article you can read here.